Ectopic EMPD

Two cases of ectopic extramammary Paget’s disease

Two cases of ectopic extramammary Paget’s disease

Extramammary Paget’s disease (EMPD) is a rare adenocarcinoma that primarily affects areas of the skin with a high presence of apocrine glands. In contrast, ectopic extramammary Paget’s disease (eEMPD) is a rarer form of EMPD that appears on areas of the skin that typically lack the presence of apocrine glands. In their 2019 review, Scarbrough et al reported a total of 45 cases of eEMPD, with only 4 cases on the face and 6 cases on the extremities. Herein, we present 2 novel cases of eEMPD—one on the posterior arm and another on the face that was initially diagnosed as melanoma in situ.